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Table 2 Diagnostic challenges in IPF

From: Idiopathic pulmonary fibrosis: diagnostic pitfalls and therapeutic challenges

Delay in diagnosis

Ruling out alternative diagnoses

Familial pulmonary fibrosis

Hypersensitivity pneumonitis

Connective Tissue Disease

Asbestosis

Sarcoidosis

Special conditions

IPF presenting as acute exacerbation of IPF

Unclassifiable ILD

Obtaining a surgical lung biopsy